Lymphangiosarcoma is a rare malignant tumour which occurs in long standing cases of primary or acquired lymphoedema. It involves either the upper or lower lymphoedematous extremities but is most common in the upper extremity.
- lymphangiosarcoma is classically seen in upper extremity lymphedema occurring after mastectomy (Stewart-Treves syndrome) (1).
This sarcoma first appears as a bruise mark, a purplish discolouration or a tender skin nodule in the extremity, typically on the the anterior surface. It progresses to an ulcer with crusting, and finally to an extensive necrosis involving the skin and subcutaneous tissue. It metastasises widely.
No effective therapy is reported.